Benjelloun, Hanane and Rachid, Safia and Rattal, Asmaa and Harraz, Hanaa and Zaghba, Nahid and Chaanoun, Khadija and Yassine, Najiba (2024) Recurrent Spontaneous Pneumothorax Revealing Marfan Syndrome: A Case Report. Journal of Advances in Medicine and Medical Research, 36 (6). pp. 291-296. ISSN 2456-8899
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Abstract
The present study reports about recurrent spontaneous pneumothorax revealing Marfan syndrome. Marfan syndrome is a rare autosomal dominant disease that affects connective tissue and affects several organs, including the lung. It appears at a variable age and can be unrefined. This is a case of patient aged 16 years, eldest of two siblings, without toxic habits, treated for pulmonary tuberculosis confirmed bacteriologically 2 years ago and operated on 5 years ago for a left inguino-scrotal hernia. The patient presented to the department on day 7 after discharge following spontaneous stabbing left chest pain associated with dyspnea at the slightest effort. On clinical examination, there was a syndrome of air effusion in the left hemithorax. The frontal chest X-ray revealed a large total left pneumothorax which was drained. Lung involvement rarely modifies the respiratory functional prognosis. The occurrence of a pneumothorax is rarely a mode of entry into the disease, hence the interest in discussing the diagnosis in cases of recurrent spontaneous pneumothorax or thoracic deformation.
Item Type: | Article |
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Subjects: | STM Digital Press > Medical Science |
Depositing User: | Unnamed user with email support@stmdigipress.com |
Date Deposited: | 08 Jun 2024 05:26 |
Last Modified: | 08 Jun 2024 05:26 |
URI: | http://publications.articalerewriter.com/id/eprint/1418 |